Skip to main content

Table 2 Distribution of pediatric patients: sex, age, Phe levels

From: Quality of Life (QoL) assessment in a cohort of patients with Phenylketonuria

Pediatric patients

Pediatric patients on BH4treatment*

Age

Sex

Phe valuesaon the day of assessment

Mean Phe valuesaover the course of the previous 12 months

I

6

F

313

292

II

10

M

416

361

III

8

F

358

350

IV

8

F

326

250

V

10

M

373

254

VI

10

F

664

553

VII

7

M

268

261

VIII

16

F

189

256

IX

6

M

254

335

X

10

F

222

224

XI

6

M

142

166

XII

11

F

240

251

XIII

16

F

309

364

XIV

16

M

251

268

XV

7

F

259

271

Pediatric patients on dietary treatment

Age

Sex

Phe values a on the day of assessment

Mean Phe values a over the course of the previous 12 months

XVI

15

M

471

318

XVII

8

M

473

343

XVIII

15

F

611

394

IXX

15

M

262

386

XX

8

M

273

291

XXI

10

F

396

320

XXII

13

F

128

476

XXIII

13

F

239

216

XXIV

9

F

288

321

XXV

16

F

563

678

XXVI

12

M

254

206

  1. *10 mg/Kg/day for each patient.
  2. aExpressed in μmol/L.