From: Quality of Life (QoL) assessment in a cohort of patients with Phenylketonuria
Pediatric patients | ||||
---|---|---|---|---|
Pediatric patients on BH4treatment* | Age | Sex | Phe valuesaon the day of assessment | Mean Phe valuesaover the course of the previous 12 months |
I | 6 | F | 313 | 292 |
II | 10 | M | 416 | 361 |
III | 8 | F | 358 | 350 |
IV | 8 | F | 326 | 250 |
V | 10 | M | 373 | 254 |
VI | 10 | F | 664 | 553 |
VII | 7 | M | 268 | 261 |
VIII | 16 | F | 189 | 256 |
IX | 6 | M | 254 | 335 |
X | 10 | F | 222 | 224 |
XI | 6 | M | 142 | 166 |
XII | 11 | F | 240 | 251 |
XIII | 16 | F | 309 | 364 |
XIV | 16 | M | 251 | 268 |
XV | 7 | F | 259 | 271 |
Pediatric patients on dietary treatment | Age | Sex | Phe values a on the day of assessment | Mean Phe values a over the course of the previous 12 months |
XVI | 15 | M | 471 | 318 |
XVII | 8 | M | 473 | 343 |
XVIII | 15 | F | 611 | 394 |
IXX | 15 | M | 262 | 386 |
XX | 8 | M | 273 | 291 |
XXI | 10 | F | 396 | 320 |
XXII | 13 | F | 128 | 476 |
XXIII | 13 | F | 239 | 216 |
XXIV | 9 | F | 288 | 321 |
XXV | 16 | F | 563 | 678 |
XXVI | 12 | M | 254 | 206 |